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An unusual case of pregnancy in a patient with Caroli’s syndrome

15 Jun 2018

Caroli´s syndrome is a rare congenital disease with an incidence of 1:1,000,000 characterized by a non-obstructive segmental cystic dilation of large intrahepatic bile ducts [1]. There are two distinguishable forms: Caroli’s syndrome, which is associated with congenital hepatic fibrosis and cirrhosis and Caroli’s disease, a much more rare condition which is linked with autosomal recessive polycystic kidney disease [2]. Caroli’s syndrome can affect young women in their childbearing age, however, due its rare incidence there is paucity of data in the literature [2–4].

Click here to view the full article which appeared in European Journal of Obstetrics & Gynecology and Reproductive Biology